通用外科杂志

  • 国际标准期刊号: 2254-6758
  • 期刊 h 指数: 8
  • 期刊引用分数: 1.33
  • 期刊影响因子: 1.34
索引于
  • Genamics 期刊搜索
  • 研究期刊索引目录 (DRJI)
  • OCLC-WorldCat
  • 欧洲酒吧
  • 谷歌学术
  • 夏尔巴罗密欧
分享此页面

抽象的

Hereditary Hemorrhagic Telangiectasia: Presenting with Epistaxis

Sandeep Kumar Kar, Manasij Mitra, Tanmoy Ganguly, Manabendra Sarkar, Chaitali Sen Dasgupta, Anupam Goswami

Osler-Weber-Rendu disease (OWRD) or Hereditary Hemorrhagic Telangiectasia (HHT) is a rare autosomal dominant disorder that causes muco-cutanesous and visceral vascular dysplasia and results in increased tendency for bleeding [1-4]. Patients with HHT may present with variety of symptoms and management differs accordingly. Epistaxis is the most common symptom of HHT and mucocutaneous telangiectasia the most common sign [5]. Here we describe the anesthesia management of a patient presenting with epistaxis in emergency suffering from this syndrome.